Cystic Fibrosis Nursing | Cystic Fibrosis Symptoms, Causes, Treatment, NCLEX Review

Cystic fibrosis NCLEX nursing review: Cystic fibrosis is a genetic disorder that causes the exocrine glands to work incorrectly.
This can lead to major complications that affect the respiratory, digestive (pancreas, liver, intestines), integumentary, and reproductive systems along with the sinuses.
What are exocrine glands? These are glands that produce and transfer it’s secretions (ex: mucous, tears, sweat, digestive enzymes) via DUCTS to it’s intended area of the body rather than directly into the bloodstream like the endocrine glands.
In cystic fibrosis, there is a gene that is mutated that prevents the exocrine gland from working properly. It is called the CFTR gene!
The CFTR gene, which stands for cystic fibrosis transmembrane regulator, is a protein that controls the channels of sodium and chloride. Hence the sodium and water transport in and out of the cell, and these channels are within the membrane of the cells that makes our sweat, mucous, tears, and digestive enzymes.
However, in CF these channels don’t work properly. Therefore, normally these channels would properly regulated sodium and water transport in and out of the cells, which helps control the flow of water within these structures among other things. But this is not what happens in a person with cystic fibrosis.
The mucous is thick and sticky rather than thin and slippery. This mucous will block the airways in the lower respiratory system and block the pancreatic duct from delivering pancreatic enzymes. In addition, the sweat glands produce excessive amounts of salt.
CF tends to affect Caucasians and males more. The current median life expectancy of a person with cystic fibrosis is 37 years of age (source: NIH.gov). It is currently diagnosed with a sweat test where pilocaprine and electric current is delivered to the skin to make it sweat. The amount of salt in the sweat is measured. Results 60 mmol/L or more is considered positive for CF.
Nursing interventions to cystic fibrosis include: chest physiotherapy (chest PT), monitor for complications, educating about PEP devices, preventing infection, administering medications and more (see the video for a detailed review of the nursing interventions)
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[@RegisteredNurseRN]

Hello Everyone!! Thank you so much for watching this video. Don't forget about: 🟣ABG eBook: registerednursern.creator-spring.com/ 🟣ABG physical book: amzn.to/3EsF0Mc (affiliate link) Quiz: www.registerednursern.com/cystic-fibrosis-nclex-questions/ Notes: www.registerednursern.com/cystic-fibrosis-nclex-review/ More Pediatric Reviews: kzbin.info/www/bejne/h3TKlIiqjNCKp6c Follow Us: Facebook: facebook.com/RegisteredNurseRNs/ Instagram: instagram.com/registerednursern_com/ Twitter: twitter.com/nursesrn

[@arceninacis7163]

great lecture video

[@mujeebgaming7912]

Hello my teacher can you please make a video on ventilator and it's complete settings plzz it's a request... I'm also a nursing student

[@CFlifestyleFoundation]

Thank you for creating such content like this! Your team is doing a great job of spreading awareness of this rare disease. Amazing job!

[@kaittoense]

I have cystic fibrosis and I’m a Labor and delivery nurse! I am so blessed to be healthy ❤️ you did a fabulous job with this video!! Hopefully many others can learn from your video and understand this disease a little better.

[@Blablablablabla31465]

Plz help how to recover.. From CF

[@nyamurungibtumusiime4562]

And i finally understand cystic fibrosis.. at this point i literally like a video even before it plays ..as long as its by you.i know its going to be great..thank you sooo much

[@Linkfan007]

Amen!

[@gr8myndse162]

EXACTLY!!!

[@maryamaboko]

I just want to say thank you so much for all you do! I used your videos throughout nursing school, and I also used them to prepare for the Nclex-RN. I passed with 75 questions. I could't have done it without God and your amazing videos!

[@janinay0766]

Hi :) I passed my NCLEX-RN last December 2017 with the help of all your videos.👍🏼 Although i'm already a passer, every once in a while I still check your videos to refresh my mind, and watching you again reminds me of my review days. :) I am recommending your channel to all my friends here in the Philippines who are going to take the exam too.. continue helping foreign nurses with your videos! God bless you sarah...❤️

[@purposewithmalika2171]

As a cfer your research was really good!!! I hate when I hear people talk about about cf that’s not accurate

[@wiseeggroll7486]

Hi Sarah, I just want to say thank you!😘 I took my nclex last week of march and passed! I’m blessed and grateful because i watched some of your videos 3 weeks before my exam😊 God bless you always!❤️🙏🏻❤️

[@wosuibian1]

To be honest, she is far more knowledgeable than some doctors

[@Skytall]

Best KZbin channel for nursing. Hands down! 🙏🏼

[@yousifmq]

Finally a channel that actually teaches, gets straight to the point and doesn't beg for likes and subscription thank you so much, liked and subscribed

[@myth8065]

Hi there Sarah! Your channel really is a blessing for me, a home care nurse adjusting in a hospital ward... If I may, it would be awesome if you could make a lecture on interpreting lab values/ecg reading... Hope you would consider.. Thanks!!

[@schonlift9027]

I love this Video! I have Cystic Fibrosis and I'm 27! Awesome! my PFT's are almost 100% however, I do have all of these issues even though my lungs are "healthy" are moving air. Bloody Sputum, Cultured Bacterias (staph, pseudo, achro, etc), Liver Issues, CFRDiabetes- Amazing how much information this video provides and it is organized beautifully.

[@johnnypatch]

Recently took the NGN-NCLEX Version. Passed the NCLEX-RN on the second try. Your videos are definitely helpful. Highly Recommended. Thank you.

[@kelseytam3521]

You've honestly helped me pass every test I've had so far. We have so much to learn and our professors don't have time to teach us everything so we are leg to learn it for ourselves. I dont learn well by just reading my books, so I correlate your information with what our books say and it helps soo much! And I learned ABGs SPECIFICALLY from your videos (not my professors)and the tic tac toe method. Thank you so much!! I appreciate you so much.

[@hannahmwangi2424]

I would like to take this opportunity and thank you for the good work you are doing . I took my Nclex last week on 27th and passed .I watched all your videos and all i can say is you are heaven sent. May God bless you abundantly. Am forever grateful.

[@user-nu3el2mo2w]

im gonna start advertising your channel to all the nursing students I know. you gotta get the credit that you deserve. all your videos are very helpful. thank you!

[@vanessyruzzle3260]

Hi nurse sarah i just want to say thank you so much for your lecture videos it really really helped me a lot in passing my nursing licensure exam here in phillipines 😊😇keep posting more nursing lecture videos.GOD BLESS YOUR FAMILY😊

[@bolt8794]

This is the greatest youtube channel I could've ever discovered!

[@coopyjay]

I had a flutter valve after my open heart surgery. It was green so everyone called it a pickle! It helped immensely! Love your videos!

[@lizzywilliams5233]

How dd u get it ryt or manage

[@donnawinsor3701]

your videos are getting me through nursing school!!! I can always count on you to explain it in a way I get! thank you so much for taking the time to do this! much appreciated !

[@chizobanweke5698]

Your the best. Please don't stop doing what you love BEST. I can only learn from your video. My professors are story tellers, no one does it best than SARAH REGISTER NURSE. 🔥🔥💕💕

[@ccthechamp9333]

Your videos are such helpful tools in breaking down the understanding of these disease processes and the role of the nurse. Thank you so much!

[@reenub2353]

Thank you so much Sara,your videos helped me to pass Nclex two weeks back,God bless,I love your teachings,still I hear it.awesome teachings

[@aleshiaedwards3089]

Your videos have gotten me through so many semesters. I'm in one of the hardest semesters and graduate May 2019 and these videos are the PERFECT refreshers to help me make the missing connections stick!

[@eugeniamulingtapang3963]

Thank you for all your videos, pathophysiology is my favorite topic. I like all your presentations because it’s comprehensive. I think I can say that just watching all of your videos is already my continuing education.

[@CreationsByWally]

As Always thanks. you really make it easy for a visual learner like me. My Professor just sat there and read out of a book.

[@r0xygirl15]

As someone who has CF, this info video is spot on. Very impressed with your understanding of my medical condition. Will use this video to educate other people on my condition, thank you.

[@ShellsBeauty]

Dude this was awesome. I like the info presented and the NCLEX questions attached (I got 100% on them). I will be using these videos by you to help me through school!

[@Jingryl]

Thanks Sarah. You such a big help for us nurses..

[@kannikaphutornlert5583]

I would like to say thank you so much for your videos. I watched your videos for my NCLEX RN and now I passed. You guy are so helpful. 🙏🙏

[@emmacalabrese5743]

you make the BEST videos and have saved my life throughout nursing school. THANK YOU!!

[@Roleplaywithray]

she is the best teacher ever know i understand whats going on thank you sara

[@bemdevelos4165]

Thank you😊 well explained .Your videos help me preparing for my incoming exam..

[@Cheerfulgiversincorporation]

Thanks and God bless you for your help.

[@anooja-dy9hy]

Thankyou Serah.. Your all lecture videos are helpful..

[@ThatGuy-sd3zl]

Very informative. I have CF as well. I wanted to learn more about the respiratory system and without realizing it you made a video about it. Subscribed.

[@damodarsingh4699]

Awesome 👌 teaching I have ever seen..please more video upload 👍👍👍🔥🔥 you are fabulous ...

[@jayjayleehoffler2555]

I wanted to thank you . I enjoy these lectures that you put on KZbin .

[@mr.baloch3587]

My Son Is Also Suffering From C.F, You Are Very Expert Sister, You Explained Very Professionally.

[@Lacilove1991]

i wish she was an instructor at my school. she breaks down so much of what the books be saying

[@jayangeles552]

me

[@vivi1989ish]

Short, simple, but yet effective your videos!! Side note, when I didn't understand a lecture in my nursing program I would just watch you videos and then I would get it! Thank you

[@Epark1801]

Thank you for the video! The information was easy to grasp(for a ninth grader at least) and was engaging.

[@gracey433]

I am preparing for my nclex exam .. this is literally a big help for me❤ thanks a lot.

[@kemmrthappy2804]

Thnks a lot .. you made me understand ths disease in just over 25mns ..thanks ..greetngs from Germany

[@shamms04]

Thank you..... am learning a lot as I prepare for my NCLEX exam from Kenya

[@fatimadiallo6947]

Omg thank you so so much you're saving my life from nursing school.❤❤❤

[@vaileybeauty]

Thank you for the great information struggling my way through med surge your videos are of great help.

[@lexshi4961]

hai mam very nice classs ..im learning every day

[@melatfesseha2552]

your videos are detail, easy to understand and helpful, thank you so much

[@nataliemartinez1313]

Honestly this video is amazing!!!! I really understand the material now. Sometimes with these videos my mind tends to wonder off but I was focused and entertained.Thank you so much!!!! Please keep making videos

[@blinkybill2997]

What an excellent lecture. Good work. THANKS!!!

[@BawsEdsy]

Well explained as always. Thanks 😘😊

[@fiesta-kimfamily3067]

Thank you, Nurse Sarah! 😊

[@dsgrts]

Thank you!!

[@adhikarideepa2104]

Thank you for such a beautiful explanations!

[@keerthibhupathiraju7060]

hey ! your videos and notes are being very helpful ! thank you soo much !!

[@noahriding5780]

I'm curious to ask when severe or chronic asthma cases are actually cystic fibrosis or something else? Thanks.

[@telelakay-tv1337]

Thank you so much your awesome work.

[@user-my4yh5fm7x]

Hi, can you please make a video about the history of nursing? I love your videos i use it as an advance reviewer. Thank you 😊

[@pravin2378]

Nice and very helpful information video

[@user-ie5gh8sr3r]

I enjoy your lectures Ma'am

[@jimhampton8098]

This was GREAT! Thank you so much!

[@caribaez5711]

Sara is a great teacher! 😇💜

[@ahlpadhasa7153]

great!!! thank you!!

[@Eddycarm]

Love your videos they have helped me soo much

[@angel01191]

thanks ! , you are so smart and have a way to explain things in such a easy way ! can't thank you enough for your work !

[@sufyanramadan4942]

incredible explanation thank you you are the best

[@Sunshine-uc6kv]

Very good for awareness of peoples

[@jaliyahmonae4306]

Since I started studying for the NCLEX, a lot of material is starting to make WAAAAY more sense than it did when I was ACTUALLY in school 🤯 THANK YOU! .. on to the next video 😁

[@julialouk9363]

I'm just finding out I had this kind of stuff and boy it hurts to breathe I have a lot of issues with the sinuses have a lot of issues with my stomach now I know why it makes sense

[@MrJimmy-ox7fq]

Excellent video (as usual!).....always learn something new an unique; great approach. Many many thanx again for your hard work and dedication; we all appreciate it!

[@angieg3143]

Cant thank you enough for these videos!

[@KL-le7xg]

Thank you!

[@NormalLifeGaming]

Great video on awareness of CF keep up the good work!!

[@sesaampanas4892]

Thanks for this video👍

[@breew5090]

I want to be a cf nurse when I'm older:)

[@BioWithMusammir]

Very well explained

[@amanhundal708]

Thankyou and love you

[@francinewintzmbbs4977]

Thank you so much!

[@tanesihaherisejohnson6288]

Thanks just doing some research on this. May be taking on an assignment with this medical condition.

[@donnagifford8733]

Thanks!

[@RegisteredNurseRN]

Thank you so much!

[@Fayeey920]

Thank you Sarah, it's excellent video.

[@dalia-h2083]

Thank you so much, so helpful 💜

[@Zaloomination]

Foun this video very helpful, thanks!

[@SalmanKhan-kx6bk]

Very well explained May God bless u

[@teressaalcantara5762]

My brother had CF he died age 5 years 10 month 1957. He was a beautiful boy I still miss him I was 6 years

[@stefenieleger]

💔🙏🏾

[@Darline562]

Amazing 😊

[@mirabellamichael7837]

Absolutely loved this

[@pinkkittybarbie9563]

Can you make a video on meningitis

[@majadbassam1032]

suchhhhh beatiful explantion ,plz do vedios about examinetion of medcine ,love you

[@RJudoo]

Hi..... Ve a question. A baby around 2 months, what he should consume if no milk content should b fed. Thx u

[@Linkfan007]

Very good review as always! Thank you Sarah! =)

[@kenedyndyamuhaki3703]

You really are amazing 🎉

[@user-pi1xh1ol1t]

Thanks alot

[@triloksingh5461]

Thanks

[@Hammorabisoldier-zg8vi]

You’re just amazing, that’s only what I can say ❤

[@shelleyrnphilippe2826]

I have my Peds final on Tuesday, I feel more confident about this topic now. Thank you so much.

[@Darline562]

Amazing

[@strongmedicose7288]

Well explained

[@mavjikatariya4936]

Thank you, very much