Von Gierke (Glycogen Storage Disease 1) for USMLE

[@hraqhraq]

Finally someone understanding pathophysiology and molecular pathology of the disease they are talking about it. Very useful. I can add that PPP is anabolic first then catabolic at the end, not just catabolic as you said, because there would be more purines synthesized and when cell senses that it will pass it to XO enzyme for catabolism

[@DocRen]

Only 2 minutes in and this makes so much more sense already. DANG THANKS

[@shantanubaghel2058]

Just wanted to say this video saved me for Step 1. Had a classic von Gierke but couldn't remember details. Thought of your pathophys breakdown and boom, got it. Thank you. Keep up the great work.

[@medicineislifeee]

omg same! After watching this, I didn't have to even read the clinical manifestations from kaplan etc. It all came to me logically!

[@reemnb1409]

manyy thanks IT WAS SUPER USEFUL

[@duaajaffar1263]

That was truly helpful thank you so much ❤️ Please keep posting more

[@zoezzz8934]

thank you!!! so clear and helpful

[@afsa2973]

Thanks a lot. You made it super easy to understand ❤️

[@osamabinkhalid4100]

You are great

[@leahodonnell9967]

Great video! Super helpful in my biochem studies, thanks!

[@ananyabasak8231]

Thanks sir it's very helpful to understand.

[@livebiochemistry]

great video

[@norma9237]

Thank you so much

[@aoi7910]

Very well explained! Amazing presentation, hope you're doing well :)

[@thestudyspot]

Thank you! You too!

[@ranonepal6851]

wonderful..thank you very very much sir...

[@jasmineouiarmaldz1935]

A huge thank u mister 👍

[@felice98]

Amazing Video! I have a question: Is the synthesis of TAGs by the liver in the fasting state for the purpose of supplying energy to the rest of the body or are they rather stored?

[@sk5869]

Damn this is so good!

[@thestudyspot]

Thanks!

[@amfarawi]

great video. 10/10.

[@ruqayasuadad3105]

thanks♥ great work

[@thestudyspot]

ruqaya suadad Your Welcome!

[@SuperCoccyx]

Thanks.It helped a lot.

[@thestudyspot]

Eugeniu Lupusor Your Welcome.

[@naveenkumar-sz1cg]

SO MUCH HELPFUL THNQ .

[@star2653]

Hi sorry this could be a stupid question but, how is there a decrease in glucose 6 phosphate? Surely there would be an increase of it because it cannot converts into glucose? You were talking about this at 8:30

[@tonyberardi1617]

He meant gluocose-6-phosphatase. It's easy to confuse so many similar sounding words lol

So glycogen builds up or no? or just the glucosa 6 phosphate?

[@rafaelgalvan4066]

Why the G6P has to be inside the ER?

[@mariaalarcon7711]

Thanks for the vid! It help me a lot

[@محمدالعنزي-س6ث7ث]

thank you ♥

[@thestudyspot]

+‫محمد العنزي‬‎ Your Welcome

[@katesn9052]

Thanks a lot! I love you

[@priscilla_7733]

Is it normal to develop a lot of food allergies as u get older? If so, why?